This formation of the platelet plug is called primary hemostasis.

这一过程即初期止血。

The formation of this platelet plug is called primary hemostasis.

这被称为初级止血过程。

The formation of the platelet plug is called primary hemostasis.

血小板栓子的形成叫做一期止血。

This is because the process called hemostasis, literally meaning to stop the flow of blood, is impaired.

这是因为血友病患者的止血过程受损，即其凝血功能出现障碍。

Normally, protein C and protein S are 2 of many proteins or enzymes that regulate the complex process called hemostasis.

通常，C和S是能调止血这一复杂过程的许和酶类的其中两种。

The main role of protein C and protein S is to prevent excess coagulation, or fibrin formation, during secondary hemostasis.

C和S的主要作用是在二期止血时防止过度凝血（即纤维形成过）。

People who suffer from disorders related to hemostasis may have trouble with unwanted clotting, or the inability to form clots.

患有与止血相关疾病的人可能会有不必要的凝血或无法形成凝块的问题。

The second factor is a state of hypercoagulation, where altered amounts of clotting factors increase primary or secondary hemostasis.

第二个因素是高凝状态，高凝状态下凝血因子数量增，会增强初期或二期凝血。

So, it has a whole system in place to prevent you from losing too much of it, through a process known as hemostasis.

所以，它有一个完整的系统来防止你失去太，通过一个被称为止血的过程。

Now, a mimic of hemophilia A is von Willebrand disease, which is an inherited problem with primary hemostasis caused by a deficiency of von Willebrand factor.

还有一种类血友病A，即血管性血友病，是一种遗传性的初级止血障碍，由血管性血友病因子（vWF）缺乏引起。

So these steps leading up to fibrin reinforcement of the platelet plug make up the process called secondary hemostasis and results in a hard clot at the site of the injury.

这一加强血小板血栓强度的过程即为二期止血，最终使得伤口上的血栓很牢固。

In the family of disorders known as hemophilia, a patient can usually complete the first two steps of hemostasis just fine, but they can't make an effective fibrin clot.

在被称为血友病的疾病家族中，病人通常可以很好地完成止血的前两个步骤，但是他们不能制造有效的纤维凝块。

In most cases of hemophilia there is a decrease in the amount or function of one or more of the clotting factors that makes secondary hemostasis less effective and allows more bleeding to occur.

在大数血友病中，都有一种或种凝血因子在数量上减少或功能上减弱，使次级止血过程的功效下降，而出血更。

To make things worse, as the clots are broken down through fibrinolysis, fibrin degradation products are released into the circulation and these interfere with platelet aggregation and clot formation, making hemostasis even more difficult.

更糟的是，当血凝块通过纤溶崩解时，纤维降解产物释放入血循环，干扰血小板聚集和血凝块形成，导致凝血更加困难。